E-ISSN 1858-8360 | ISSN 0256-4408
 

Case Report 


Aplasia cutis congenita of extremities (group VII): case report from North-Western Nigeria

Sanni Abiola Usman, Lawal Olatunde Taslim, Muhammad Ibrahim Habib, Musa Tawakaltu Lily (1), Olateju Eyinade Kudirat, Audu Isah Lamidi.

Online Publishing Date: 24 / 01 / 2024


Abstract
Aplasia cutis congenita (ACC) is a rare congenital disorder characterized by localized or widespread absence of skin mainly affecting the scalp. Bilateral involvement of both the upper and lower extremities is uncommon. This is a case report of a rare congenital disorder. The patient was a 26-hour-old male baby admitted with extensive absence of skin of the lower and upper extremities. He was co-managed conservatively with the plastic surgical team for ACC group VII. The lesions were healing satisfactorily until 12 days into the admission when the parents signed against medical advice despite counseling. Aplasia cutis congenita with involvement of both upper and lower extremities is a rare presentation which responds to conservative treatment. The report emphasizes the need for a legal frame work for physicians to override the decision of the care giver not in the best interest of a child.

Key words: Aplasia cutis congenital, extremities, group 7, Nigeria.


 
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How to Cite this Article
Pubmed Style

Usman SA, Taslim LO, Habib MI, () MTL, Kudirat OE, Lamidi AI. Aplasia cutis congenita of extremities (group VII): case report from North-Western Nigeria. Sudan J Paed. 2023; 23(2): 234-238. doi:10.24911/SJP.106-1670856184


Web Style

Usman SA, Taslim LO, Habib MI, () MTL, Kudirat OE, Lamidi AI. Aplasia cutis congenita of extremities (group VII): case report from North-Western Nigeria. https://sudanjp.com//?mno=93801 [Access: February 06, 2024]. doi:10.24911/SJP.106-1670856184


AMA (American Medical Association) Style

Usman SA, Taslim LO, Habib MI, () MTL, Kudirat OE, Lamidi AI. Aplasia cutis congenita of extremities (group VII): case report from North-Western Nigeria. Sudan J Paed. 2023; 23(2): 234-238. doi:10.24911/SJP.106-1670856184



Vancouver/ICMJE Style

Usman SA, Taslim LO, Habib MI, () MTL, Kudirat OE, Lamidi AI. Aplasia cutis congenita of extremities (group VII): case report from North-Western Nigeria. Sudan J Paed. (2023), [cited February 06, 2024]; 23(2): 234-238. doi:10.24911/SJP.106-1670856184



Harvard Style

Usman, S. A., Taslim, . L. O., Habib, . M. I., (), . M. T. L., Kudirat, . O. E. & Lamidi, . A. I. (2023) Aplasia cutis congenita of extremities (group VII): case report from North-Western Nigeria. Sudan J Paed, 23 (2), 234-238. doi:10.24911/SJP.106-1670856184



Turabian Style

Usman, Sanni Abiola, Lawal Olatunde Taslim, Muhammad Ibrahim Habib, Musa Tawakaltu Lily (), Olateju Eyinade Kudirat, and Audu Isah Lamidi. 2023. Aplasia cutis congenita of extremities (group VII): case report from North-Western Nigeria. Sudanese Journal of Paediatrics, 23 (2), 234-238. doi:10.24911/SJP.106-1670856184



Chicago Style

Usman, Sanni Abiola, Lawal Olatunde Taslim, Muhammad Ibrahim Habib, Musa Tawakaltu Lily (), Olateju Eyinade Kudirat, and Audu Isah Lamidi. "Aplasia cutis congenita of extremities (group VII): case report from North-Western Nigeria." Sudanese Journal of Paediatrics 23 (2023), 234-238. doi:10.24911/SJP.106-1670856184



MLA (The Modern Language Association) Style

Usman, Sanni Abiola, Lawal Olatunde Taslim, Muhammad Ibrahim Habib, Musa Tawakaltu Lily (), Olateju Eyinade Kudirat, and Audu Isah Lamidi. "Aplasia cutis congenita of extremities (group VII): case report from North-Western Nigeria." Sudanese Journal of Paediatrics 23.2 (2023), 234-238. Print. doi:10.24911/SJP.106-1670856184



APA (American Psychological Association) Style

Usman, S. A., Taslim, . L. O., Habib, . M. I., (), . M. T. L., Kudirat, . O. E. & Lamidi, . A. I. (2023) Aplasia cutis congenita of extremities (group VII): case report from North-Western Nigeria. Sudanese Journal of Paediatrics, 23 (2), 234-238. doi:10.24911/SJP.106-1670856184





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