E-ISSN 1858-8360 | ISSN 0256-4408
 

Case Report 


Unusual sites of Rosai-Dorfman disease in children: 5 years’ experience from tertiary care pediatric hemato-oncology center

Janani Aru, Riya Kataria, Varsha Kolli, Arunan Murali, Gramani Arumugam Vasugi, Arathi Srinivasan.

Abstract
Rosai-Dorfman disease (RDD) is a rare histiocytic disorder, usually presenting with massive lymphadenopathy. The involvement of extra nodal sites, bone and nodal sites like mediastinum are rare. Clinical data of three cases of extra nodal RDD who were admitted in our Pediatric Hemato-oncology unit were analyzed in the last 5 years. The extra nodal RDD (maxillary sinus, nasal pharyngeal focus, and external auditory meatus) were diagnosed based on histopathology and positron emission tomography (PET) scan. They were treated with steroids, but were refractory hence requiring salvage chemotherapy. Currently all 3 of them are in complete remission. Extra nodal RDD are difficult to diagnose, and histopathology and radiology play an important role. Here we present three cases, of which two were steroid refractory which were treated with salvage chemotherapy and are in complete remission.

Key words: Extra nodal, Rosai Dorfman disease, Children, Fluorodeoxyglucose Positron Emission Tomography.


 
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How to Cite this Article
Pubmed Style

Aru J, Kataria R, Kolli V, Murali A, Vasugi GA, Srinivasan A. Unusual sites of Rosai-Dorfman disease in children: 5 years’ experience from tertiary care pediatric hemato-oncology center. Sudan J Paed. 2022; 22(1): 109-115. doi:10.24911/SJP.106-1623391582


Web Style

Aru J, Kataria R, Kolli V, Murali A, Vasugi GA, Srinivasan A. Unusual sites of Rosai-Dorfman disease in children: 5 years’ experience from tertiary care pediatric hemato-oncology center. https://www.sudanjp.com/?mno=87326 [Access: August 01, 2022]. doi:10.24911/SJP.106-1623391582


AMA (American Medical Association) Style

Aru J, Kataria R, Kolli V, Murali A, Vasugi GA, Srinivasan A. Unusual sites of Rosai-Dorfman disease in children: 5 years’ experience from tertiary care pediatric hemato-oncology center. Sudan J Paed. 2022; 22(1): 109-115. doi:10.24911/SJP.106-1623391582



Vancouver/ICMJE Style

Aru J, Kataria R, Kolli V, Murali A, Vasugi GA, Srinivasan A. Unusual sites of Rosai-Dorfman disease in children: 5 years’ experience from tertiary care pediatric hemato-oncology center. Sudan J Paed. (2022), [cited August 01, 2022]; 22(1): 109-115. doi:10.24911/SJP.106-1623391582



Harvard Style

Aru, J., Kataria, . R., Kolli, . V., Murali, . A., Vasugi, . G. A. & Srinivasan, . A. (2022) Unusual sites of Rosai-Dorfman disease in children: 5 years’ experience from tertiary care pediatric hemato-oncology center. Sudan J Paed, 22 (1), 109-115. doi:10.24911/SJP.106-1623391582



Turabian Style

Aru, Janani, Riya Kataria, Varsha Kolli, Arunan Murali, Gramani Arumugam Vasugi, and Arathi Srinivasan. 2022. Unusual sites of Rosai-Dorfman disease in children: 5 years’ experience from tertiary care pediatric hemato-oncology center. Sudanese Journal of Paediatrics, 22 (1), 109-115. doi:10.24911/SJP.106-1623391582



Chicago Style

Aru, Janani, Riya Kataria, Varsha Kolli, Arunan Murali, Gramani Arumugam Vasugi, and Arathi Srinivasan. "Unusual sites of Rosai-Dorfman disease in children: 5 years’ experience from tertiary care pediatric hemato-oncology center." Sudanese Journal of Paediatrics 22 (2022), 109-115. doi:10.24911/SJP.106-1623391582



MLA (The Modern Language Association) Style

Aru, Janani, Riya Kataria, Varsha Kolli, Arunan Murali, Gramani Arumugam Vasugi, and Arathi Srinivasan. "Unusual sites of Rosai-Dorfman disease in children: 5 years’ experience from tertiary care pediatric hemato-oncology center." Sudanese Journal of Paediatrics 22.1 (2022), 109-115. Print. doi:10.24911/SJP.106-1623391582



APA (American Psychological Association) Style

Aru, J., Kataria, . R., Kolli, . V., Murali, . A., Vasugi, . G. A. & Srinivasan, . A. (2022) Unusual sites of Rosai-Dorfman disease in children: 5 years’ experience from tertiary care pediatric hemato-oncology center. Sudanese Journal of Paediatrics, 22 (1), 109-115. doi:10.24911/SJP.106-1623391582





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